ePrints

A prospective study of the presentation and management of dancing eye syndrome/opsoclonus-myoclonus syndrome in the United Kingdom

Lookup NU author(s): Dr Ki Pang

Downloads

Full text for this publication is not currently held within this repository. Alternative links are provided below where available.

Abstract

The incidence, mode of presentation and management of Dancing Eye Syndrome/Opsoclonus-Myoclonus Syndrome (DES/OMS) was prospectively evaluated in 20 United Kingdom (UK) paediatric neurology centres by questionnaire over a 24-month period between 2003 and 2005 Nineteen children were notified, giving an incidence of 0 18 cases per million total population per year Mean age at presentation was 18 months (range 3-42 months) Fifteen families consented to participate in the study Atypical features were present in 6/15 cases including very delayed presentation of opsoclonus, dysphagia, and rapid spontaneous improvement without treatment Only 4/15 cases were associated with neuroblastoma (NB) but current practice in excluding this is diverse and a standardised approach is suggested (C) 2009 European Paediatric Neurology Society Published by Elsevier Ltd All rights reserved

Publication metadata

Author(s): Pang KK, de Sousa C, Lang B, Pike MG

Publication type: Article

Publication status: Published

Journal: European Journal of Paediatric Neurology

Year: 2010

Volume: 14

Issue: 2

Pages: 156-161

ISSN (print): 1090-3798

ISSN (electronic): 1532-2130

Publisher: Elsevier Ltd

URL: http://dx.doi.org/10.1016/j.ejpn.2009.03.002

DOI: 10.1016/j.ejpn.2009.03.002

Altmetrics

Share